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Revista chilena de pediatría

versión impresa ISSN 0370-4106

Resumen

DIDIER CRUZ A, Israel; BARON L, Sara; GARRIDO G, Claudia  y  VELAZQUEZ S, Jose Roberto. Childhood Sarcoidosis. A rare pediatric disease: Case report. Rev. chil. pediatr. [online]. 2011, vol.82, n.6, pp.535-541. ISSN 0370-4106.  http://dx.doi.org/10.4067/S0370-41062011000600009.

Sarcoidosis is a systemic disease of unknown etiology. It affects various organs, including skin, eyes, joints, liver, heart, spleen and lymph nodes. Lungs are the organs most affected by this disorder and while symptomatology may vary thoughout life, most likely it is never diagnosed. It appears to be endemic in countries like England, US and Japan. The incidence is low in Mexico and Latin America. There is a genetic predisposition, where histocompatibility has a significant role. Histopathological diagnosis requires the presence of non-caseificating granulomatous lesions, with epiteloid cells with cytoplasmatic inclusions called Schaumann cells; these are diagnostic. The most severe complication is pulmonary fibrosis, which responds to steroids. We present the case of a schoolage child who was diagnosed as suffering from sarcoidosis after an open lung biopsy. Treatment with systemic steroids was initiated and is currenty asymptomatic, under observation and without complications secondary to treatment.

Palabras clave : Pulmonary sarcoidosis; mediatinal adenopathies; children.

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