SciELO - Scientific Electronic Library Online

 
vol.76 número4Síndrome hemofagocítico secundario en pediatría: Experiencia clínica en ocho casos índice de autoresíndice de materiabúsqueda de artículos
Home Pagelista alfabética de revistas  

Servicios Personalizados

Revista

Articulo

Indicadores

Links relacionados

Compartir


Revista chilena de pediatría

versión impresa ISSN 0370-4106

Resumen

MUNOZ B., Eliana et al. Juvenile dermatomyositis. Rev. chil. pediatr. [online]. 2005, vol.76, n.4, pp.404-409. ISSN 0370-4106.  http://dx.doi.org/10.4067/S0370-41062005000400011.

Introduction: Juvenile dermatomyositis is an idiopathic multisystemic disease characterized by striated muscle and skin inflammation. There is limited information about this entity in Chile. Objective: Describe clinical features, therapy and outcome of patients with Juvenile Dermatomyositis in Santiago, Chile. Methods: A retrospective study including all patients with diagnosis of juvenile dermatomyositis belonging to Hospital Clínico Universidad Católica and Hospital Sótero del Río between 1993 and 2003. Results: 9 girls and 2 boys were included with median age at diagnosis of 8 years-old. The interval between onset of symptoms and diagnosis was median 5 months and average follow-up period was 2 years (interval 6 months-58 months). The most common findings at onset were weakness and a characteristic skin rash. All patients were treated with steroids and 73% cases received metotrexate. At the end of the study, 73% of all patients achieved disease-remission. Conclusions: Favourable outcome of most patients could be related to early diagnosis and the use of inmunosuppressor agents

Palabras clave : Juvenile Dermatomyositis; miopathy; clinical features; laboratory; therapy.

        · resumen en Español     · texto en Español

 

Creative Commons License Todo el contenido de esta revista, excepto dónde está identificado, está bajo una Licencia Creative Commons