SciELO - Scientific Electronic Library Online

vol.136 issue10C1q nephropathy: Report ofone caseGastric adenocarcinoma appearing 32 years after the resection of a gastric lymphoma. Report of one case author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand




Related links


Revista médica de Chile

Print version ISSN 0034-9887


RADULESCU, Dan et al. A rare case of primitive right atrium angio-sarcoma with favorable outcome, in a young female: Case report and literature review. Rev. méd. Chile [online]. 2008, vol.136, n.10, pp.1311-1316. ISSN 0034-9887.

Primary malignant cardiac tumors are extremely rare, but their associated mortality is very high. The clinical presentation is oñen variable and nonspecific; by the time symptoms appear, the tumor has usually evolved to a large intracardiac and paracardiac mass causing considerable hemodynamic involvement, regional invasión and distant dissemination. We report a 26 year-old female with a right atrium angiosarcoma with a surprisingly favorable outcome at 2 years follow-up after treatment with a combination of neoadjuvant chemotherapy and surgical resection. She presented with chest tightness, shortness of breath at effort, atypical chest pain, palpitations, asthenia, weight loss and profuse perspiration. Physical examination and irnaging diagnostic procedures, identified a pericardial effusion and a pathologic cardiac mass. The diagnosis of a malignant angiosarcoma was suggested afier computed tomography transthoracic and transesophageal echocardiography It was confirmed at surgery by a biopsy followed by histopathology and immunohistochemistry.

Keywords : Chemotherapy, adjuvant; Echocardiography; transesophageal; Hemangiosarcoma; Heart neoplams; Pericardial effusion.

        · abstract in Spanish     · text in English     · English ( pdf )


Creative Commons License All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License