Revista chilena de cirugía
versão On-line ISSN 0718-4026
GAMBOA C, CRISTIAN et al. Hepatectomy for cholangiocarcinoma in one patient with Dubin Johnson syndrome. Rev Chil Cir [online]. 2009, vol.61, n.3, pp. 279-284. ISSN 0718-4026. doi: 10.4067/S0718-40262009000300011.
Dubin-Johnson syndrome (SDJ) is a rare benign autosomal recessive congenital disease that causes jaundice. We report a 71 years old male with a Dubin Jonson syndrome diagnosed at the age of 40. On a ultrasound examination and magnetic resonance imaging, a liver tumor was found, that was excised. The pathology report showed a cholangiocarcinoma. During the postoperative period, the patient had a hyperbilirubinemia that subsided slowly. There are reports of hyperbilirubinemia of difficult management after hepatectomy in patients with Dubin-Johnson syndrome.
Palavras-chave : Dubin Johnson; hepatectomy; cholangiocarcinoma.