Resumen

DIAZ G, JUAN C et al. Results of surgical treatment of Caroli disease . Rev Chil Cir [online]. 2008, vol.60, n.1, pp. 10-16. ISSN 0718-4026.  doi: 10.4067/S0718-40262008000100004.

Background: Caroli disease is a congenital sacular dilatation of intrahepatic bile tract. Aim: To report a series of patients with Caroli disease. Material and methods: Retrospective review of medical records of patients with a pathological diagnosis of Caroli disease, operated in a surgical service, between 1994 and 2005. Results:\Ne report 18 patients aged 50 + 14 years (11 women). The main presentation symptom was abdominal pain in 16 patients (89%). The disease was localized in 16 patients (in the left lobe in 14 and in the right lobe in 2) and generalized in two. The most common findings in abdominal ultrasound or CAT scan, were intrahepatic bile tract dilatation, intrahepatic lithiasis and cystic images. The diagnosis was confirmed by endoscopio retrograde colangiography in six patients and magnetic resonance of the bile tract in four. Seventeen patients were subjected to a segmentectomy and one to a cyst resection. Mean operative time and hospital stay were 3.4 hours and 8.7 days, respectively. No patient died. Patients were followed for a mean of 30 months and in one, the disease reappeared in the contralateral lobe. Conclusions: Partial hepatectomy is a definitive treatment for localized Caroli disease, with a low incidence of complications and mortality

Palabras clave : Caroli disease; colestasis; segmentectomy.